[A case of Churg-Strauss granulomatous angiitis: an autonomous clinical entity or a variant of panarteritis nodosa?].
Minerva Med, 1978/10/13;69(48):3311-8.
PMID: 31578
Impact factor: 5.58
Abstract
A fatal case of Churg and Strauss granulomatous angiitis in a 21-yr-old woman is described. Its unusual features included marked personal and familial dysreaction, sudden onset, bronchopulmonitis with distinct eosinophilia and antibiotic- and cortisone-resistant pericarditis, and a terminal picture of generalised septico-pyaemia. The histological findings included necrotising systemic vasculitis with granulomas, some of them extravascular, in various organs. Differential diagnosis and the relation between this form and panarteritis nodosa are discussed.
MeSH terms
Adult; Diagnosis, Differential; Female; Humans; Polyarteritis Nodosa; Pulmonary Eosinophilia; Vasculitis
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